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DeCS
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Descriptor English:
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Glutaryl-CoA Dehydrogenase
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Descriptor Spanish:
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Glutaril-CoA Deshidrogenasa
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Descriptor Portuguese:
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Glutaril-CoA Desidrogenase
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Synonyms English:
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CoA Dehydrogenase, Glutaryl
Dehydrogenase, Glutaryl CoA
Dehydrogenase, Glutaryl-CoA
Dehydrogenase, Glutaryl-Coenzyme A
Glutaryl CoA Dehydrogenase
Glutaryl Coenzyme A Dehydrogenase
Glutaryl-Coenzyme A Dehydrogenase
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Tree Number:
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D08.811.682.660.425
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Definition English:
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A flavoprotein enzyme that is responsible for the catabolism of LYSINE; HYDROXYLYSINE; and TRYPTOPHAN. It catalyzes the oxidation of GLUTARYL-CoA to crotonoyl-CoA using FAD as a cofactor. Glutaric aciduria type I is an inborn error of metabolism due to the deficiency of glutaryl-CoA dehydrogenase. |
History Note English:
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2006(1973)
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Allowable Qualifiers English:
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Record Number:
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50627
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Unique Identifier:
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D050770
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Occurrence in VHL:
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Similar:
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DeCS
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